GLUTARYLCARNITINE
| 中文名称 | GLUTARYLCARNITINE |
|---|---|
| 中文同义词 | 戊二酰基肉碱;谷氨酰-L-肉碱锂盐;谷氨酰- |
| 英文名称 | Glutaroyl carnitine |
| 英文同义词 | Glutaroyl carnitine;Glutaroyl N-(methyl-D3)-carnitine;(L)-Glutaryl Carnitine;(2R)-3-Carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-triMethyl-1-propanaMiniuM Inner Salt;DL-Glutaryl Carnitine;L-Glutaryl Carnitine
DISCONTINUED. Please see G597605;Glutamyl- |
| CAS号 | 102636-82-8 |
| 分子式 | C12H21NO6 |
| 分子量 | 0 |
| EINECS号 | |
| 相关类别 | Chiral Reagents;Intermediates & Fine Chemicals;Metabolites & Impurities;Pharmaceuticals;Chiral Reagents, Metabolites & Impurities, Pharmaceuticals, Intermediates & Fine Chemicals |
| Mol文件 | 102636-82-8.mol |
| 结构式 |  |
GLUTARYLCARNITINE 性质
| 储存条件 | 2-8°C |
|---|---|
| 溶解度 | 可溶于二甲基亚砜、甲醇、水 |
| 形态 | 凝胶 |
| 颜色 | 透明无色 |
| 旋光性 (optical activity) | [α]/D -20±2°, c = 1 in H2O |
| 稳定性 | 非常吸湿 |
Glutarylcarnitine 丙二酸尿症和 I 型戊二酸尿症的重要诊断代谢物。
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Human Endogenous Metabolite
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Malonylcarnitine and Glutarylcarnitine are important diagnostic metabolites in the screening of dried blood spots by tandem mass spectrometry.
The urinary excretion of glutarylcarnitine is a specific biochemical marker of glutaric acidemia type I (GA-1). The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I.