Glutaroyl carnitine 化学特性,用途語,生産方法
化学的特性
Clear Thick Gel
使用
A metabolite of L-Carnitine (C184110).
Biochem/physiol Actions
Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.
Glutaroyl carnitine 上流と下流の製品情報
原材料
準備製品