Glutaroyl carnitine

Glutaroyl carnitine 구조식 이미지
카스 번호:
102636-82-8
상품명:
Glutaroyl carnitine
동의어(영문):
Glutaroyl carnitine;DL-Glutaryl Carnitine;(L)-Glutaryl Carnitine;Glutaroyl N-(methyl-D3)-carnitine;L-Glutaryl Carnitine DISCONTINUED. Please see G597605;(2R)-3-Carboxy-2-(4-carboxy-1-oxobutoxy)-N,N,N-triMethyl-1-propanaMiniuM Inner Salt
CBNumber:
CB31565246
분자식:
C12H21NO6
포뮬러 무게:
0
MOL 파일:
102636-82-8.mol
MSDS 파일:
SDS

Glutaroyl carnitine 속성

저장 조건
2-8°C
용해도
DMSO, 메탄올, 물에 용해됨
물리적 상태
색상
투명 무색
optical activity
[α]/D -20±2°, c = 1 in H2O
안정성
흡습성이 매우 높음

안전

Glutaroyl carnitine C화학적 특성, 용도, 생산

화학적 성질

Clear Thick Gel

용도

A metabolite of L-Carnitine (C184110).

Biochem/physiol Actions

Increased formation and excretion of glutarylcarnitin results from a glutaryl-CoA dehydrogenase deficiency, an inborn error of lysine and tryptophan metabolism. Secondary carnitine depletion due to increased formation and urinary excretion of glutarylcarnitine is suggested to play an important role in the neuropathogenesis of glutaryl-CoA dehydrogenase deficiency, inducing excitotoxic neuronal damage and mitochondrial dysfunction.

Glutaroyl carnitine 준비 용품 및 원자재

원자재

준비 용품


Glutaroyl carnitine 공급 업체

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