L-A-HYDROXYGLUTARIC ACID DISODIUM)

L-A-HYDROXYGLUTARIC ACID DISODIUM) 구조식 이미지
카스 번호:
63512-50-5
상품명:
L-A-HYDROXYGLUTARIC ACID DISODIUM)
동의어(영문):
L-2-HG;SKL187;Disodium (S)-2-hydroxyglutarate;(S)-2-Hydroxypentanedioic acid;Sodium (S)-2-hydroxypentanedioate;L-2-Hydroxyglutarate DisodiuM Salt;L-α-Hydroxyglutaricaciddisodiumsal;L-2-Hydroxyglutaric acid (disodium);(S)-2-Hydroxyglutaric acid disodium;L-ALPHA-HYDROXYGLUTARIC ACID DISODIU
CBNumber:
CB81473690
분자식:
C5H9NaO5
포뮬러 무게:
172.11
MOL 파일:
63512-50-5.mol
MSDS 파일:
SDS

L-A-HYDROXYGLUTARIC ACID DISODIUM) 속성

녹는점
>300°C
저장 조건
2-8°C
용해도
메탄올(매우 소량), 물(미량)에 용해됨
물리적 상태
고체
물리적 상태
단단한 모양
색상
흰색에서 황백색까지
optical activity
[α]/D -8.5±1.5°, c = 1 in 0.1 M NaOH
BRN
5318042

안전

WGK 독일 3

L-A-HYDROXYGLUTARIC ACID DISODIUM) C화학적 특성, 용도, 생산

개요

L-α-Hydroxyglutaric acid (L-2-HG) is an α-hydroxy acid. It is metabolized to 2-oxoglutarate (α-ketoglutarate) by L-2-hydroxyglutarate dehydrogenase, and mutations in this enzyme lead to 2-hydroxyglutaric aciduria, a neurometabolic disorder characterized by increased L-2-HG levels. L-2-HG is structurally similar to α-ketoglutarate and competitively inhibits α-ketoglutarate-dependent dioxygenases, including several involved in histone lysine and DNA demethylation.

화학적 성질

White Solid

용도

A potential inhibitor of glutamate carboxypeptidase.

일반 설명

Glutamic acid is metabolized to α-Hydroxyglutaric acid in an NAD-dependent manner by cell-free extracts of Peptococcus aerogenes. It is formed as an intermediate during glyoxylic acid metabolism in bacteria.

L-A-HYDROXYGLUTARIC ACID DISODIUM) 준비 용품 및 원자재

원자재

준비 용품


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