| Company Name: |
Sigma-Aldrich
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| Tel: |
021-61415566 800-8193336 |
| Email: |
orderCN@merckgroup.com |
| Products Intro: |
Product Name:Ornithine Transcarbamylase
CAS:9001-69-8
Purity:lyophilized powder, main >= 300units/mg protein Package:30units, 300units Remarks:O2501
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| Company Name: |
Creative Enzymes
|
| Tel: |
1-516-855-7709 |
| Email: |
info@creative-enzymes.com |
| Products Intro: |
Product Name:Native Streptococcus faecalis Ornithine Transcarbamylase
CAS:9001-69-8
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| Company Name: |
Riedel-de Haen AG
|
| Tel: |
800 558-9160 |
| Email: |
|
| Products Intro: |
CAS:9001-69-8
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| | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Basic information |
| Product Name: | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE | | Synonyms: | EC 2.1.3.3;CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE;ORNITHINE TRANSCARBAMYLASE;ORNITHINE CARBAMYLTRANSFERASE;ornithine carbamoyl transferase from strept. faec.;ornithine carbamyltransferase from*streptococcus;Carbamoyltransferase, ornithine;ORNITHINE CARBAMYLTRANSFERASE FROM*STREP TOCOCCUS FA | | CAS: | 9001-69-8 | | MF: | | | MW: | 0 | | EINECS: | 232-625-1 | | Product Categories: | | | Mol File: | Mol File | ![CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Structure]() |
| | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Chemical Properties |
| storage temp. | −20°C | | form | lyophilized powder |
| | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Usage And Synthesis |
| Description | An enzyme that catalyzes the transfer of a carbamyl
group from carbamyl phosphate to ornithine to form citrulline; it is a constituent reaction of the urea cycle. This enzyme normally
occurs in the mitochondria of liver cells, but only to a minute extent
in serum. Since it does not occur to a significant extent in serum,
kidney, brain, etc., and only 1% or 2% of the hepatic concentration
occurs in small intestine, its presence in serum is a specific indica_x0002_tion of damage to liver cells. | | Biochem/physiol Actions | Mutations in ornithine transcarbamylase cause Ornithine transcarbamylase deficiency which prevents the clearance of the byproduct ammonia leading to hyperammonemia. |
| | CARBAMOYLPHOSPHATE: L-ORNITHINE CARBAMOYLTRANSFERASE Preparation Products And Raw materials |
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